{"id":140,"date":"2025-04-28T17:42:32","date_gmt":"2025-04-28T17:42:32","guid":{"rendered":"https:\/\/honeydew-hyena-350809.hostingersite.com\/?page_id=140"},"modified":"2025-05-08T14:49:21","modified_gmt":"2025-05-08T14:49:21","slug":"about-spg3a","status":"publish","type":"page","link":"https:\/\/kidswithspg3a.com\/ko\/about-spg3a\/","title":{"rendered":"SPG3A \uc815\ubcf4"},"content":{"rendered":"<div style=\"height:100px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<h1 class=\"wp-block-heading\" id=\"spastic-paraplegia-3a\ub780-\ubb34\uc5c7\uc778\uac00\">SPASTIC PARAPLEGIA 3A\ub780 \ubb34\uc5c7\uc778\uac00?<\/h1>\n\n\n\n<p>SPG3A(\ub610\ub294 ATL1-HSP\ub85c\ub3c4 \uc54c\ub824\uc9d0)\ub294 \uc5b4\ub9b0\uc774\ub4e4\uc5d0\uac8c \uac00\uc7a5 \ud754\ud55c \uc0c1\uc5fc\uc0c9\uccb4 \uc6b0\uc131 HSP \uc720\ud615\uc785\ub2c8\ub2e4. SPG3A\uc758 \ud3c9\uade0 \ubc1c\ubcd1 \uc5f0\ub839\uc740 4\uc138\uc774\uba70, 80% \uc774\uc0c1\uc758 \uc0ac\ub840\uac00 10\uc138 \uc774\uc804\uc5d0 \uc99d\uc0c1\uc744 \ubcf4\uc785\ub2c8\ub2e4.<br><br>SPG3A\ub294 \uc720\uc804\uc131 \uacbd\uc9c1\uc131 \ud558\ubc18\uc2e0 \ub9c8\ube44\ub77c\ub294 \ud76c\uadc0 \uc2e0\uacbd \uc9c8\ud658 \uadf8\ub8f9\uc758 \ud558\uc704 \uc720\ud615\uc785\ub2c8\ub2e4. \uc720\uc804\uc131 \uacbd\uc9c1\uc131 \ud558\ubc18\uc2e0 \ub9c8\ube44\ub294 \uc885\uc885 \ub450 \uac00\uc9c0 \uc720\ud615\uc73c\ub85c \ub098\ub269\ub2c8\ub2e4: \uc21c\uc218\ud615\uacfc \ubcf5\ud569\ud615. \uc21c\uc218\ud615\uc740 \ud558\uccb4\uc5d0\ub9cc \uc601\ud5a5\uc744 \ubbf8\uce58\uba70, \ubcf5\ud569\ud615\uc740 \uc0c1\uc9c0 \ubc0f \uad6c\uac15 \uc6b4\ub3d9 \uadfc\uc721\uacfc \uac19\uc740 \uc2e0\uccb4\uc758 \ub2e4\ub978 \ubd80\uc704\uc5d0\ub3c4 \uc601\ud5a5\uc744 \ubbf8\uce58\uba70, \ubc1c\uc791 \ubc0f \uc9c0\uc801 \uae30\ub2a5 \ubcc0\ud654\uc640 \uac19\uc740 \ub2e4\ub978 \uc99d\uc0c1\uc744 \ub3d9\ubc18\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4.<br><br>ATL-1(Atlastin-1) \uc720\uc804\uc790\uc758 \ub3cc\uc5f0\ubcc0\uc774\ub294 SPG3A\ub97c \uc720\ubc1c\ud569\ub2c8\ub2e4. \uc774\ub7ec\ud55c \ub3cc\uc5f0\ubcc0\uc774\ub294 \uc544\ud2c0\ub77c\uc2a4\ud2f4-1\uc758 \ube44\uc815\uc0c1\uc801\uc778 \ud65c\ub3d9\uc744 \uc720\ub3c4\ud558\uc5ec \ub274\ub7f0\uc758 \uae30\ub2a5, \ud2b9\ud788 \uc138\ud3ec \ub0b4 \ubb3c\uc9c8 \ubd84\ud3ec\ub97c \uc190\uc0c1\uc2dc\ud0ac \uac00\ub2a5\uc131\uc774 \ub192\uc2b5\ub2c8\ub2e4. \uae30\ub2a5\uc801 \uc544\ud2c0\ub77c\uc2a4\ud2f4-1 \ub2e8\ubc31\uc9c8\uc758 \ubd80\uc871\uc740 \ub610\ud55c \ucd95\uc0ad\uc758 \uc131\uc7a5\uc744 \uc81c\ud55c\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \ub300\ub1cc\ud53c\uc9c8\ucc99\uc218\ub85c\uc758 \uae34 \ub274\ub7f0 \ub0b4\uc5d0\uc11c \uc774\ub7ec\ud55c \ubb38\uc81c\ub294 \uc138\ud3ec \uc0ac\uba78\ub85c \uc774\uc5b4\uc9c8 \uc218 \uc788\uc2b5\ub2c8\ub2e4. \uadf8 \uacb0\uacfc, \ub274\ub7f0\uc740 \uc2e0\uacbd \ucda9\ub3d9\uc744 \uc804\ub2ec\ud560 \uc218 \uc5c6\uc73c\uba70, \ud2b9\ud788 \ud558\uccb4\uc758 \ub2e4\ub978 \ub274\ub7f0\uacfc \uadfc\uc721\uc5d0 \uc804\ub2ec\uc774 \uc5b4\ub824\uc6cc\uc9d1\ub2c8\ub2e4. \uc774\ub7ec\ud55c \uc2e0\uacbd \uae30\ub2a5 \uc7a5\uc560\ub294 \uacbd\uc9c1\uc131 \ud558\ubc18\uc2e0 \ub9c8\ube44 3A\ud615\uc758 \uc9d5\ud6c4\uc640 \uc99d\uc0c1\uc744 \ucd08\ub798\ud569\ub2c8\ub2e4.<br><br>SPG3A\ub97c \uac00\uc9c4 \ub300\ubd80\ubd84\uc758 \uac1c\uc778(>95%)\uc740 \uc601\ud5a5\uc744 \ubc1b\uc740 \ubd80\ubaa8\ub97c \uac00\uc9c0\uace0 \uc788\uc2b5\ub2c8\ub2e4. \uc989, \uc801\uc5b4\ub3c4 \ud55c \uba85\uc758 \ubd80\ubaa8\ub85c\ubd80\ud130 \uc720\uc804\uc790 \ub3cc\uc5f0\ubcc0\uc774\ub97c \ubb3c\ub824\ubc1b\uc2b5\ub2c8\ub2e4. \uc77c\ubd80 \uac1c\uc778\uc5d0\uc11c\ub294 \ub3cc\uc5f0\ubcc0\uc774\uac00 &#8220;\ub4dc \ub178\ubcf4(de novo)&#8221;\ub85c \ubc1c\uc0dd\ud558\uba70, \uc989 \ubc30\uc544 \ubc1c\ub2ec \uc911\uc5d0 \uc720\uc804\uc790\uac00 \ubb34\uc791\uc704\ub85c \ub3cc\uc5f0\ubcc0\uc774\ub97c \uc77c\uc73c\ucf1c \ubd80\ubaa8\ub85c\ubd80\ud130 \uc720\uc804\ub418\uc9c0 \uc54a\uc2b5\ub2c8\ub2e4.<\/p>\n\n\n\n<p>\ucd9c\ucc98: \uad6d\ub9bd\ubcf4\uac74\uc6d0, \uad6d\ub9bd\uc758\ud559\ub3c4\uc11c\uad00, MedlinePlus<\/p>\n\n\n\n<figure class=\"wp-block-image size-full\"><img loading=\"lazy\" decoding=\"async\" width=\"1784\" height=\"1081\" src=\"https:\/\/kidswithspg3a.com\/wp-content\/uploads\/2025\/04\/635b6516ec84c0032d42e584_Rectangle-50-min.png\" alt=\"\" class=\"wp-image-141\" title=\"\" srcset=\"https:\/\/kidswithspg3a.com\/wp-content\/uploads\/2025\/04\/635b6516ec84c0032d42e584_Rectangle-50-min.png 1784w, https:\/\/kidswithspg3a.com\/wp-content\/uploads\/2025\/04\/635b6516ec84c0032d42e584_Rectangle-50-min-300x182.png 300w, https:\/\/kidswithspg3a.com\/wp-content\/uploads\/2025\/04\/635b6516ec84c0032d42e584_Rectangle-50-min-1024x620.png 1024w, https:\/\/kidswithspg3a.com\/wp-content\/uploads\/2025\/04\/635b6516ec84c0032d42e584_Rectangle-50-min-768x465.png 768w, https:\/\/kidswithspg3a.com\/wp-content\/uploads\/2025\/04\/635b6516ec84c0032d42e584_Rectangle-50-min-1536x931.png 1536w\" sizes=\"auto, (max-width: 1784px) 100vw, 1784px\" \/><figcaption class=\"wp-element-caption\">\ucd9c\ucc98: Arun Meyyazhagan \ubc15\uc0ac\uc758 \uc720\uc804\uc131 \uacbd\uc9c1\uc131 \ud558\ubc18\uc2e0 \ub9c8\ube44: \uc5c5\ub370\uc774\ud2b8<\/figcaption><\/figure>","protected":false},"excerpt":{"rendered":"<p>SPASTIC PARAPLEGIA 3A\ub780 \ubb34\uc5c7\uc778\uac00? SPG3A(\ub610\ub294 ATL1-HSP\ub85c\ub3c4 \uc54c\ub824\uc9d0)\ub294 \uc5b4\ub9b0\uc774\ub4e4\uc5d0\uac8c \uac00\uc7a5 \ud754\ud55c \uc0c1\uc5fc\uc0c9\uccb4 \uc6b0\uc131 HSP \uc720\ud615\uc785\ub2c8\ub2e4. SPG3A\uc758 \ud3c9\uade0 \ubc1c\ubcd1 \uc5f0\ub839\uc740 4\uc138\uc774\uba70, 80% \uc774\uc0c1\uc758 \uc0ac\ub840\uac00 10\uc138 \uc774\uc804\uc5d0 \uc99d\uc0c1\uc744 \ubcf4\uc785\ub2c8\ub2e4. SPG3A\ub294 \uc720\uc804\uc131 \uacbd\uc9c1\uc131 \ud558\ubc18\uc2e0 \ub9c8\ube44\ub77c\ub294 \ud76c\uadc0 \uc2e0\uacbd \uc9c8\ud658 \uadf8\ub8f9\uc758 \ud558\uc704 \uc720\ud615\uc785\ub2c8\ub2e4. \uc720\uc804\uc131 \uacbd\uc9c1\uc131 \ud558\ubc18\uc2e0 \ub9c8\ube44\ub294 \uc885\uc885 \ub450 \uac00\uc9c0 \uc720\ud615\uc73c\ub85c \ub098\ub269\ub2c8\ub2e4: \uc21c\uc218\ud615\uacfc \ubcf5\ud569\ud615. \uc21c\uc218\ud615\uc740 \ud558\uccb4\uc5d0\ub9cc \uc601\ud5a5\uc744 \ubbf8\uce58\uba70, \ubcf5\ud569\ud615\uc740 \uc0c1\uc9c0 \ubc0f [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"ghostkit_customizer_options":"","ghostkit_custom_css":"","ghostkit_custom_js_head":"","ghostkit_custom_js_foot":"","ghostkit_typography":"","footnotes":""},"class_list":["post-140","page","type-page","status-publish","hentry"],"blocksy_meta":{"background":{"background_type":"image","background_pattern":"type-1","background_image":{"attachment_id":142,"x":0,"y":0,"url":"https:\/\/kidswithspg3a.com\/wp-content\/uploads\/2025\/04\/635bd3421cfdc0509b3cd923_Artboard-min.png"},"gradient":"linear-gradient(135deg,rgba(6,147,227,1) 0%,rgb(155,81,224) 100%)","background_repeat":"repeat","background_size":"auto","background_attachment":"scroll","patternColor":{"default":{"color":"#e5e7ea"}},"overlayColor":{"default":{"color":"CT_CSS_SKIP_RULE"}},"backgroundColor":{"default":{"color":"#ffffff"}}},"styles_descriptor":{"styles":{"desktop":"[data-prefix=\"single_page\"] {background-position:0% 0%;background-color:#ffffff;background-image:url(https:\/\/kidswithspg3a.com\/wp-content\/uploads\/2025\/04\/635bd3421cfdc0509b3cd923_Artboard-min.png);}","tablet":"","mobile":""},"google_fonts":[],"version":6},"has_hero_section":"disabled"},"_links":{"self":[{"href":"https:\/\/kidswithspg3a.com\/ko\/wp-json\/wp\/v2\/pages\/140","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/kidswithspg3a.com\/ko\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/kidswithspg3a.com\/ko\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/kidswithspg3a.com\/ko\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/kidswithspg3a.com\/ko\/wp-json\/wp\/v2\/comments?post=140"}],"version-history":[{"count":13,"href":"https:\/\/kidswithspg3a.com\/ko\/wp-json\/wp\/v2\/pages\/140\/revisions"}],"predecessor-version":[{"id":194,"href":"https:\/\/kidswithspg3a.com\/ko\/wp-json\/wp\/v2\/pages\/140\/revisions\/194"}],"wp:attachment":[{"href":"https:\/\/kidswithspg3a.com\/ko\/wp-json\/wp\/v2\/media?parent=140"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}